Anesthetic experience of patient with isolated left ventricular noncompaction: a case report

نویسندگان

  • Doyeon Kim
  • Eunhee Kim
  • Jong-Hwan Lee
  • Chung Su Kim
  • Sangmin Maria Lee
  • Jung Eun Lee
چکیده

Isolated left ventricular noncompaction (LVNC) is a rare primary genetic cardiomyopathy characterized by prominent trabeculation of the left ventricular wall and intertrabecular recesses. Perioperative management of the patient with LVNC might be challenging due to the clinical symptoms of heart failure, systemic thromboembolic events, and fatal left ventricular arrhythmias. We conducted real time intraoperative transesophageal echocardiography in a patient with LVNC undergoing general anesthesia for ovarian cystectomy.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Ventricular noncompaction in a female patient with nephropathic cystinosis: a case report

INTRODUCTION We report an unusual and interesting case of a 24-year-old woman with nephropathic cystinosis in association with concomitant isolated noncompaction of the left ventricle. Left ventricular noncompaction usually presents with reduced exercise tolerance as a consequence of ventricular dysfunction, the result of embolus or with palpitations and syncope due to arrhythmia. There is no s...

متن کامل

Case report: Ablation of diffuse inter-trabecular substrate in a patient with isolated ventricular non-compaction.

We present the case of an 18-year old male with a history of isolated noncompaction of the ventricular myocardium (INVM). The patient was originally diagnosed at age 14, following a collapse at school when intermittent complete heart block was seen on ECG. A cardiac MRI at this time showedmild noncompaction of the entire left ventricular (LV) free wall and the distal third of the septum, mild d...

متن کامل

Biventricular Noncompaction Cardiomyopathy in a Patient Presenting with New Onset Seizure: Case Report

Ventricular noncompaction (VNC) of the myocardium is a rare genetic cardiomyopathy caused by a disorder during endocardial morphogenesis and could be accompanied by life-threatening complications. The major clinical manifestations of VNC are heart failure, arrhythmias, and embolic events. The left ventricle is the most commonly reported affected site, but a few cases of right ventricular involv...

متن کامل

Exercise-Induced Right Ventricular Outflow Tract Tachycardia in a Patient with Isolated Left Ventricular Noncompaction

Isolated left ventricular noncompaction is a hereditary cardiomyopathy in which a variety of supraventricular and ventricular arrhythmias could be observed. We report a patient with exercise-induced ventricular tachycardia with left bundle branch block morphology that had characteristics of an idiopathic ventricular tachycardia who was subsequently diagnosed as left ventricular noncompaction. S...

متن کامل

'Idiopathic' acute myocardial infarction in a young patient with noncompaction cardiomyopathy.

Isolated left ventricular noncompaction (LVNC) is a rare hereditary cardiomyopathy characterized by prominent intraventricular trabeculations separated by deep intertrabecular recessus. While cardiac ischemia due to microvascular dysfunction is common in these patients, ST-segment elevation myocardial infarction (STEMI) is rare and usually seen as a consequence of coincidental coronary artery d...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:

دوره 69  شماره 

صفحات  -

تاریخ انتشار 2016